产品说明
生化/生理作用
2-Methylbutyryl-L-carnitine is not usually detected in normal individuals. The elevation of 2-methylbutyrylcarnitine suggests a deficiency of a dehydrogenase specific for isobutyryl-CoA, important in the differential diagnosis of branched chain organic acidurias by analysis of urinary organic acids and acylcarnitines in plasma or dried blood spots.
基本信息
经验(实验)分子式 | C12H23NO4 |
分子量 | 245.32 |
Beilstein | 5946881 |
MDL编号 | MFCD11975299 |
PubChem化学物质编号 | 329757597 |
NACRES | NA.26 |
产品性质
质量水平 | 100 |
测定 | ≥97.0% (HPLC) |
形式 | powder or crystals |
旋光性 | [α]/D -20±2°, c = 0.1 in H2O |
杂质 | ≤10% water |
颜色 | white to off-white |
储存温度 | 2-8℃ |
SMILES string | C[N+](C)(C)C[C@H](OC(C(CC)C)=O)CC([O-])=O |
InChI | 1S/C12H23NO4/c1-6-9(2)12(16)17-10(7-11(14)15)8-13(3,4)5/h9-10H,6-8H2,1-5H3/t9?,10-/m1/s1 |
InChI key | IHCPDBBYTYJYIL-QVDQXJPCSA-N |
安全信息
储存分类代码 | 13 - Non Combustible Solids |
WGK | WGK 3 |
闪点(F) | Not applicable |
闪点(C) | Not applicable |
Sigma-Aldrich