产品说明
生化/生理作用
Isovalerylglycine is a byproduct of the catabolism of the amino acid leucine. Accumulation of isovalerylglycine occurs in Isovaleric Acidemia (IVA), an autosomal recessive disorder caused by mutations in the isovaleryl-CoA dehydrogenase gene. The deficiency of this enzyme in the metabolism of leucine leads to the accumulation of a series of isovaleryl-CoA metabolites, such as isovalerylglycine (IVG).
基本信息
经验(实验)分子式 | C7H13NO3 |
分子量 | 159.18 |
Beilstein | 1766622 |
MDL编号 | MFCD00059629 |
PubChem化学物质编号 | 329756342 |
NACRES | NA.26 |
产品性质
质量水平 | 100 |
测定 | ≥97.0% (GC) |
形式 | powder or crystals |
颜色 | white to off-white |
mp | 87-90 ℃ |
格式 | neat |
InChI | 1S/C7H13NO3/c1-5(2)3-6(9)8-4-7(10)11/h5H,3-4H2,1-2H3,(H,8,9)(H,10,11) |
InChI key | ZRQXMKMBBMNNQC-UHFFFAOYSA-N |
安全信息
储存分类代码 | 11 - Combustible Solids |
WGK | WGK 3 |
闪点(F) | Not applicable |
闪点(C) | Not applicable |
Sigma-Aldrich