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Rabbit anti-SMN1 Antibody, Affinity Purified

品牌
Sigma-Aldrich
货号
PLA0219
规格纯度
Powered by Bethyl Laboratories, Inc.
参考价格
5699.93 *本价格含增值税费
促销
服务
  • 原厂保证
  • 包邮
  • 增值税票
数量
-+
产品名称:
Rabbit anti-SMN1 Antibody, Affinity Purified
SMA@
Component of Gems 1
BCD541
Kugelberg-Welander disease)
SMN
SMA3
Gemin-1
survival motor neuron 1 protein
SMA4
SMA1
SMA
SMA2
TDRD16A
tudor domain containing 16A
GEMIN1
T-BCD541
spinal muscular atrophy (Werdnig-Hoffmann disease
SMNT
产品介绍:

产品说明

免疫原

The epitope recognized by PLA0219 maps to a region between residue 244 and 294 of human survival of motor neuron 1 using the numbering given in entry NP_000335.1 (GeneID 6606).

外形

Tris-citrate/phosphate buffer, pH 7 to 8 containing 0.09% Sodium Azide

其他说明

Survival motor neuron protein (SMN1) has been identified as the gene that is defective in spinal muscular atrophy (SMA), a neurodegenerative autosomal recessive disease characterized by paralysis and muscular atrophy which results from the loss of motor neurons in the spinal cord. There are two closely related SMN genes that do not appear to be functionally redundant. SMN1 represents the telomeric copy while SMN2 represents the centromeric copy. In the cell, SMN1 is part of a large complex of proteins involved in snRNP biogenesis. The functional role of SMN1 is proposed to play a role in messenger and ribosomal RNA transcription and processing.

免责声明

Unless otherwise stated in our catalog or other company documentation accompanying the product(s), our products are intended for research use only and are not to be used for any other purpose, which includes but is not limited to, unauthorized commercial uses, in vitro diagnostic uses, ex vivo or in vivo therapeutic uses or any type of consumption or application to humans or animals.

基本信息

NACRESNA.41

产品性质

生物来源rabbit
质量水平100
抗体形式affinity purified immunoglobulin
antibody product typeprimary antibodies
等级Powered by Bethyl Laboratories, Inc.
species reactivityhuman
technique(s)immunoprecipitation (IP): 2-5 μg/mg
western blot: 1:2,000- 1:10,000
登记号NP_000335.1
运输wet ice
储存温度2-8℃
Gene Informationrabbit ... SMN1(6606)

安全信息

储存分类代码12 - Non Combustible Liquids
WGKnwg

Sigma-Aldrich

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